3. Old stuff
          3.2. Old physio stuff (around 2005)
              3.2.7. Disease
                  Genetic
                      Cystic fibrosis
 Investigation [Cystic fibrosis] 

Investigation
[Cystic fibrosis]

Chest X-ray

  • Increased interstitial reticular markings
  • Bronchietasis
  • Hilar adenopathy
  • Upper lobes are more involved than lower lobes

Lung function tests

  • Obstructive pattern

Culture and sensitivity of the sputum

Diagnosis

Diagnosis is confirmed with
   -> sweat test (sweat Na+ >60mmol/L)

If sweat test is abnormal, diagnosis is confirmed.

If the sweat test is normal, but clinically the diagnosis is still suspected, then do genetic testing to confirm/exclude diagnosis.

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